CASE REPORT
Year : 2022  |  Volume : 16  |  Issue : 2  |  Page : 217-220

Perioperative total intravenous anesthesia in a child with Walker-Warburg syndrome: A case report


1 Department of Anesthesia and Critical Care, Faculty of Medicine, King Abdulaziz University; Anesthesiology Services Section, King Abdulaziz University Hospital, King Abdulaziz University, Jeddah, Saudi Arabia
2 Department of Anesthesia and Critical Care, Faculty of Medicine, King Abdulaziz University; Anesthesiology Services Section, King Abdulaziz University Hospital, King Abdulaziz University; Clinical Skills and Simulation Centre, Vice presidency of Development, King Abdulaziz University, Jeddah, Saudi Arabia

Correspondence Address:
Wadeeah Bahaziq
Department of Anaesthesia and Critical Care, Faculty of Medicine, King Abdulaziz University, P.B. Box 80215, Jeddah - 21589
Saudi Arabia
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/sja.sja_529_21

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Purpose: Walker-Warburg syndrome is a rare autosomal recessive congenital muscular dystrophy presenting with hydrocephalus, type II lissencephaly, cerebellar malformation, and ocular anomalies. Here, we describe the use of perioperative total intravenous anesthesia in a pediatric patient with Walker-Walburg syndrome. Clinical Features: A 2-month-old girl with Walker-Walburg syndrome was admitted for urgent ventriculoperitoneal shunt insertion. Anesthesia was induced using intravenous atropine (100 μg), ketamine (10 mg), and fentanyl (15 μg). The patient was monitored for various clinical parameters based on American Society of Anesthesiologists standards. Anesthesia was maintained using intermittent doses of 0.5 mg intravenous midazolam and 5–10 μg fentanyl in incremental boluses. The postoperative course was uneventful. Conclusions: To our knowledge, no published cases have reported the use of total intravenous anesthesia in patients with Walker-Walburg syndrome who have potential risks for anesthetic-induced malignant hyperthermia. This report described the key features, potential anesthetic management plan, and current literature review of Walker-Walburg syndrome.


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