| CASE REPORT |
|
| Year : 2023 | Volume
: 17
| Issue : 1 | Page : 83-86 |
|
|
Anesthetic challenges in the management of Larsen syndrome: A rare congenital anomaly
Subhasree Das1, Aparajita Panda2, Sritam S Jena2, Mantu Jain3
1 Department of Trauma and Emergency, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
2 Department of Anesthesiology and Critical Care, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
3 Department of Orthopedics, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India
Correspondence Address:
Subhasree Das
Department of Trauma and Emergency, All India Institute of Medical Sciences Bhubaneswar, Odisha - 751 019
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/sja.sja_518_22
|
|
|
Larsen syndrome is a rare inherited disease associated with dislocations of multiple joints, typical syndromic facies, and multiple spine abnormalities. They often required multiple corrective orthopedic surgeries to regain their functional ability, thus needing repeated anesthesia. Apart from skeletal deformities, they have predicted difficult airway and need extreme care during intubation and positing of the patient. Abnormal posturing due to spinal deformity and poor pulmonary reserve due to kyphoscoliosis creates an extremely challenging situation for the anesthetist to manage the case during the perioperative period. Here we are describing the perioperative anesthetic management of a patient with Larsen syndrome.
|
|
|
|
| [FULL TEXT] [PDF]* |
|
 |
|
